                          ˿µϣ20080702գ

08.07.02, ӡܻǲܣǸ⡷
08.07.02, StrongϺѪҺоԺʿСм١
08.07.02, ѰйҪƶȡ
08.07.02, Źҫԡ۴סԭ֤ݵĳ
08.07.02, ԨҶעӪװ
08.07.02, ޴ģ
08.07.02, ڹȻѧĿеʦǷӦûرԼѧĿ?
08.07.02, 󡶶ûй𣡡
08.07.02, ǰ¶үүҽ˼
08.07.02, Сθҽ۽֡
08.07.02, ڶӡ֮йɫڶ̼
08.07.02, ҵԼ2008걱ѧѧԺҵ´
08.07.02, ־顶Ӹ۴󡰺ͺС⿴ڵشѧĲࡷ
08.07.02, wangjianѧġӴ߽ѧ
08.07.02, ᰮǳʵ·ľдһ˵
08.07.02, թɧ һֻûͶSP̱
08.07.02, ʫѡʱľɰ

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                      ܻǲܣǸ

                          ӡ

    봨ʱһϿεķѧʦȫѧ
ԼܵٳºýʦعⲢ绤һ顣
±ûʲôġѧУʦδСѧļ໤
ˣбѧȫΣѽʱѧܶΥ
ְҵ¡ôڵʱһεĽʦӦôǷ
˵ӦøϿѧһܣ

    ڵѧУȱⷽĽԴֻƾűӦ
ܷӦȴδؾͶԡѧУȻһ㶼ƶϸİȫƻ
ԽʦҪӦԸ˾Ĺ涨ƽʱϰ׼
Щ涨ʱѧϿΣʦӦ
ص̨棬Զ봰ڣֶ60룬Ȼӽɢ

    ݵֲźͺʮֻȻרҽ飬
ڻץסȴȻʱǵıܷӦ
ܵ⣬ôױĵơ񡢵ӻ
ʯˡרҵĽڣ㵽̨ȼӲļ
ߵ£ץסҾߣֹͣ뿪ΧûпڻļҾߣ
͵ǽǣ²ڻͷʱ˯ڴϣ
ͷͷպڳڳﲻҪ

    Щÿ˴СͶ֪νʶͼ
սʶһλе񡤿յ˾ʹ󳪷о
մͳܵʸߴ98ǣ컨
ǿʱὫ̨ȼҾ߻򳵶ѹ٣˻ᱻѹ
ǣӦԵƶڼӲļҾ߻Աߣ컨бѹڼ
ߡϣһȡռ䣬ܰʽ
2

    յѾȶӶӳ˵ȫ缸ʮش
ѵľֹȥΪȨЩ˵ܹ㡣
봨֮󣬹Ҳ׷õʼתν
Ѿȶӡͷȥܴʵֻ
һ֯յҲֵûɡԳ911ֲ¼ʱ
óĵľԮ˻65Ԫ˺⳥Ǿý
ĵ飬֤ݱŦԼľԮȥֻΪ
¼ۣթ˾顣

    ܿյʵʲôȥƺ
е󣬵ȷڷĳЩطγܹ
ԮԱʱЩطҴߡڣЩνġ
ڵ֮γɵģжڷĸط֡
ս㵽䡢ԱߣǷ
˾ռأʵοǡǡ෴յĽ˹ؼһ
㣺ǿʹ컨嵹ʱ䡢Ҳᷢ
ƶԱ߷ܻܿᱻЩѹ

    ķݰҪ󶼱һĿܣ
С𲻻ޡ𲻵ʹ俹𼶱Ĵ
ȻԷش𺦣һҲᵹµ
Ϊݵģ󲿷Ǿŵͼ
ܵʱ׹ҵˤ򱻵ϲƵµġʱ
ȫΪʲôٷСѵʱҪ
ıܣڻץסȴ

    ȷڵķпƶҲǶ̣
ȫѡ񡣵ݲпܣһ͵أܣ
ͻᱻڵײ㣬Ӧðܳȥ¥ϣ
ܻûüܳȥ¥̮ˣޱرǾͱȶ㵽
̨ٱҪöࡣܻǲܣʱôѡģ
رǵڵķݵĿܺĵʱ

    ͷٿһʼᵽġܡ¼ѧĽѧ¥ûе
ɼ俹ܲô£ѡͺˣҪ
ܣҪ㡣ǳڽʦѧΣΪԼİȫ
ܡǲӦõġ

2008.6.29.

й걨2008.7.2

(XYS20080702)

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ϺѪҺоԺʿСм

ߣStrong

ʿã

ż˿ʵ𾪹ôѧרǽܳҲǣ
浽ѧܺ١ΪһٴҽƽʱӴҪǲˣû뵽
ȴ˹֪ϺѪҺоڹʷҲܴƫʵ
ٵΪһǹѪҺѧרҡԺʿоɹ

ԼƽʱĶףֻڼλйNotch1ܰ
ѪԼԤõı󣬲ȥףܸ˷йѧ߷
£

Zhu YM, Zhao WL, Fu JF, Shi JY, Pan Q, Hu J, Gao XD, Chen B, Li JM, 
Xiong SM, Gu LJ, Tang JY, Liang H, Jiang H, Xue YQ, Shen ZX, Chen Z, 
Chen SJ. NOTCH1 mutations in T-cell acute lymphoblastic leukemia: 
prognostic significance and implication in multifactorial 
leukemogenesis. Clin Cancer Res. 2006 May 15;12(10):3043-9. 

رϸĶȫģӦϺѪҺоĳԺʿСĹ
notch1ͻǳ˼ܰϸѪԤһ
ۡʱֻǾᵽĳ˰ѪƵҩյƽ׶
the induction course was VDCP regimen administered over a 4-week 
period (vincristine 1.5 mg/m2, days 1, 8, 15, and 22; daunorubicin 30 
mg/m2 or idarubicin 9 mg/m2, days 1-3; cyclophosphamide 800 mg/m2, 
days 1 and 8; prednisone 60 mg/m2, days 1-28). A supplement dose of 
6,000 IU/m2 L-asparaginase every other day was added on days 15 to 29 
when bone marrow blasts persisted >5% on day 14. The patients then 
received a course combining cytorabine (1 g/m2 every 12 hours, days 1-4) 
with mitoxantrone (10 mg/m2, days 3-5).  ƽ׶consolidation 
therapy of all the patients included three cycles of high-dose 
methotrexate regimen (methotrexate 3-5 g/m2 for 1 day every 10 days, 
three courses continuously), one cycle of VDLDex regimen (same dosage 
of vincristine and daunorubicin/idarubin on days 1 and 8, with 
L-asparaginase 6,000 IU/m2 every other day on days 2-12 and 
dexamethasone 6 mg/m2 per day on days 1-14), followed by one cycle of 
EA regimen (etoposide, 300 mg/m2, cytarabine, 300 mg/m2, days 1, 4, 
and 7). Ƽڹ⻹б棬ںٲãҲδѧ
ϺѪҺоڵҽԺ

ʱҲδ⣬Ϊ볢һƵƣֻǲģԺ
ιڵѧϣ͹ڸҽԺҽԺҽЩ
ƣϣҽǶδù˸߼Ʒٺ
ͨżڼѪҺоƵػ˽Ϻûа
ơϢֻ˵ĵƷʱ
ƼֻΪùϵרϿϺѪҺо
ǿȺ͹Ƚˮƽһ£ǵѧ۵㡣Σ
ǲȷġΪܻ󵼶ȥͬơ֪ʿԴ
ο?

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йҪƶ

Ѱ

߷һٴйϵȱʧһ˹Ȼƭڣ
ƵƵ֣йΪȡĴʩƭ
ߣ·˽ƣƭ߾Ȼù·ˣЩо
Ľͷåʲô·ƽѾץӡ

߷һһԵĶᾭ÷չȦƭԲ
ԼǷֶξۼƸĲƸΪκв
ǷֶεԴֱӵв뾭ϴ
Է˵Щȡò˶ȡϸķʽֱ
ԵᾭóɱԽԽߣƭ߿ԲⱵӶ޹ĲƸһ
ڴ·ƽߡһ壬ְԶ
ʱҪڲдļȵƭ˻๴ᣬıȡ
ߡ

ĵȦһӦʱȡжֲ
©ģôаЧ棬ƭߵ
ɱйƵƵֵαѧרҡթ˵ȿظߵ
Ӧȡѵһ˲ٷͰλıúܣ
ʵȴӶȱЧϵƽ棬ִ
ΪĪǰɿջ

һϵУӦרŵִϵĲΪ
ȡ֤ĵͼƭۣͲҪ̫ĵ뾫
ͿԳɹϣ׷ΡȻһ˾ϵҲ
ġ

ΣʹùԴʼҪЧ棬еǱڵ
Ϊܹõ飬һ۴ף
ٵʿ۸ϲıȡɱӪ10%
мǮʿﻹƸõƯŮзԱô
ںϷǷıԵپ漰Ч⣬һСģѹ
ϷȨˣеͲʵڵظ
ϵӦԺԼߣ֮һͿǼ
ϣClass Action

νϣΪϹ̳ɱ߰ԺҪѴľ
ӦҲдԴɱģΪ˽Լɱԭ߱水һ
ĹƶȺϲϣһȻŵ٣ô
ʹķˣͿδʵֳŵظ棬еһظ棬
Ի۰ģ˷ɱϰ

ɱϰָԭ߱棬ԤϽԶڷ
ظ棬ѡϣöԷսʤһ
10Σÿ100ԪʹʤߣҲ޷ǻԭѷõĲټһ
ĳͷԲй2000Ԫ߷ʱ
׼ظ棬пظ棬ɱԶ4000Ԫ߲ĻԶ
ᷢظ棬ĿûйоԣЮ
ҵΪڵɱϰʱҲнϸ߳ɱթһȺߣ
ǱڵĲ˾ͿЮȺвκһߡ

ϣᵼ´ԭȺˣʵ
ղȡһȵķáĳһߣԸ
Ŀ߷ϣˣͻмĳɱֻԼ
߶ĲǣӮˣߵĲгȡ
һĴã1500ˣƽһ4Σÿ100Ԫô
ԭѷôﵽ60ԪϳͷԲ120ԪΪߴ
ĳ׿ȡ20%Ĵã24һ޴ľô̼
򲻷

ڼϵĹңʵϺܶʦѰĴᣬ
ͨ򲻷ҵ

ԵƭΪйʹǣҲһֲǡ
ϵʵйϵУдƵĲϵ
ϵзϵһСԵΪйִţ繤ֳ̾
棬ǿƹرյսɷǷã⵱ȻǱڵĵߣ
źǣʧְδܱߣֻϵùթ
ã˹ֵַ̾˼άйţϲ
ȨҽʦͽսɷǷõš

һǲʵģΪйڽ˼١δ
бߵΣƭƭãֱԼ
ôΪǷųһһƭӣһײ
ƭӵĻȻûƭãƭڽм١һķ
ϵУӦ߾ȡرƭƲʧ
߲ĳͷйķƻйƭѺ״̬
ĲΪأмٵľ޴ʵ

йӦΪͨڴ칫ƽƶȣһᣬ
ܻĻᣬǳͱѹʧߴ
άȨĻᣬΪƼٴյĻᡣԶԱ
ƶǿϲϵƶȽ衣

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ԡ۴װԭ֤ݵĳ

Źҫ

æѾܾûп˿ˡ4Ѯ֪ǹ
˾ˡһֱſͥӡ˿֪ڿͥˡһοͥԺ
͸ֱΪܺãɴһʹӰù
һЩ

ղϸ鿴ֱԭṩ֤ݡҸеǳźȡ
ѧչʷϾ̱塱ĿѧңȻʹ÷֤ݵʱ
ó֤28Ȼûһɱֵ֤

ʹ1998ꡣҰ˼ҴһƼ˾Էó100֤
ݡʲôֽ쵼ʾĳĳ쵼ĺӰ֤
ӡһѡҿԺ100֤ݡУֻһ֤ݾսԡ
ǰûиᵽ֤漰顣ҵĵԺ
ҸֻҪƷһ֤ݣ֤ݶ֮

ҵĵ˸Ͻѷ֤ϴҡȻԺͥԺƷ
ɱﵼֵ֤ݣʹöԷ100֤ȫ˷ֽ

Ҹеǳźڡ˾ṩġ֤ݡУҵ
սԵ֤ݾȻûһ

жϣ¼

һڵҶֲٺзֲϸ롰۴ס޹ءΪ
ͬɹñȰ˹̹˹ЧӦڰ˹̹
˼ⷢ˾óо桢Ӱ񡢻֤ͱֽ֤ݣ
ֻ֤1986ӡڵȷڵҶֲٺзֲϸ
롰۴סʲôϵ˵Щ֤ݵ֤
㡣

ڶ֤92007˼άʵҡⱨ桷ֻ֤
׿ԿǣĴֲϸʲô
ϵⱨ桷жϡñ̲Ҳп
õʵȥ⣬ҲܼƵĽǲ˵
̲Ŀֲϸ֤7ķҲһ


֤17֤19ֻ֤ҶֲҽЧ
֤۴סҲЧΪֲͬĶң
ıֻи۲ֵûٴͳ塣֤22֤23䷨
Ҳˡ

ġ֤24֤25̸ǿڷ绯øе⣬
롰۴ס޹ϵ

塢֤27ֱЦ֤ͼ֤йԱѵĳԹ
Ӫסʵڲ⣬йԱѵĳԹӪ׾
˵ʲôʵӳԹĶϰûгԹϰճԹĶʵ
ҲδسԹ˭֤Щ֪ĻʵӳԹĶһǺö
أ 

ӷѧĽǶ˵۴סУӦṩ֤ǣ
۴סβôḻSODģҲ˵ͨʵ
;ʹͨױӪʵ֤ó֤ݼֵԳ
ǰ֤ݡ֪˾ܲóֵ֤òһ
ǣ֤ݻڶ±ظ֤ݵ֤ҲΪġ

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ҶעӪװ

ߣԨ
Դ»

ʿϹ˾ˡǱó׹˾20
ԭǷӽýɷʱ˵ǹ˾CEBӪǼٵġ
ֽϻֱӹϵҺҶע

˾ִ׸SODÿʳö൱ڿ
4000άE˵νCEBϸӪش׫ʣҲ
κӪֵǷԺѾʼ˰ڷͥϣӵʦ˵
㡣һתͨʹˮʵCEBӪأ
ڶ˾ƸüѾһƻѯʵ
ִƷûͨ󶨣ڷǷӪ

гϡ߿ƼʳƷӪƷƷ廨ţɽ
඼һЩӢĸдҲ˵컨׹ΪһƼäҵ
취ǽסڴһž֮⡣һ򵥵ĵǵ
½ء߽ɭ߳ɭ֮ǰڳΪ֮ǰ˹ԼڳΪ
֮200ûгӪƷǸӪƷúܺã
60ںңҽΪҩʳֻҪϹ߲ˣ
мѼ⣬ƫʳӪ㹻ˣòƷǸƷġݣ
һͷҪġ

˵CEBӪףͬжαֻܰȶ죬ڴ
ҹעӡִ׹繫˾ʮ˵ã
лĽһס룬һ
һģǺ鸣죿֤Ǽٵģڶ׵
ҲʡǮңҲԱ¶ڹ컯֮£Ըƹ˵
滷Ҳһ¡һҪ飬һ֤٣йزһҪ׷
ΣЧȣη塣ýҪһ߳ӷ
۹£񡰴򻢡һӰ죬ˡ

ҳƭӡ30ǰϹһεһȥгˣ·
һͿһЩڻҵŮҰۡ˵ǹɽģ
ЧΧмۣ˵Ұκãѵá
ҿһûаգ߿ˡ֪ʲôʱһǳʵ긾
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ȥԼã͸ַҲǺõġҿһۣʮֳʵ֣
֮ٵġƶũǷأʮ飬һ顣ؼһ
С飬ڱϿˮһ״һ׷ζ
еһ֮£ҽһ鶫ӽͨ¡¡ص
ײ㡣Ϊ˺ü죬Ҫ֪ʱҵĹʲʮǮ

ӴˣҾȷˡڴսԷ롣ʵгãҵ
թΪӴ˷ĳ֣һ¡꣬οϢһձ
˵̸˵гСѧѧʹѧȲͬչ׶ΣСѧ׶Σ
ͬ١̸¡ع˸ĸ￪30һҾ
ͻͽһҵһһҡֱ죬ҹгδ
ѧҵթȴ˴ѧѲùͿСŮ
ǽڿѧ֮࣬һǴԣƯĵͼⲻǴѧˮƽ
ʲô

зŭΪֻߵùÿٲƷ
¶ҶǳǳԸǳֻͬʱڴʿ
ʮֵľ⡣ͼʲôʲôҲͼȫƾһǻƾŶ
ߺĸ

ıҶԷӣѾ˹ޡȻҲ
ѧƾʶҲ֪һγ4000άEֱǷ裬Ȼǡ
ڡ˭˭ҪԺоǶעɡ

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޴ģ



615գ봨ɶʻ̳ϣпԺԺʿBڵ
һ仰봨ʹؿǾۼõͷţδڳ
ٷ˼ϵĴ𣬳ɶٿ԰ȫϡĴ
⵽һЩ˻ɺͷԣзáģһ˲࣬
˿²١ҷںѶ͵ġBԺʿʱҹ񿴿ѧ
йı103Ϊαѧ
ǰ7޳ҵĹ۵㡣ڱ𴦣ԺʿЩе
ҲĻ⣬ǲ֪ڳɶٷ˼ϵĴ
ģ뵽ýһԺʿģҲ֪е
һĵ˽⡣

1975ǱġʴУ21⡰Ϊʲôеʱڵǿң
еʱԼľ⣬ǵʽǰάдġ
˵һڵʹؿǾۼһͷŵˣٷ
͵ԽҪʱԽҲöô
֪Ҫʱ䡣̹ʵĽʲôѧĹʽԼ㣬Ǹʷ
ϵĵ¼ͳƳġǾԵģݲôȷҲ˭
ֱϣҪдʵΪҽĵʹǣ
ܽϵһ𣬶Եص㡣ڿ˹
ºרŴ绰˱ĵѧҺѧңбصͳѧǣ
ǹЦ֮࣬˵ЦǸĿƵĲ֪ѧ۵Ա
ʽֿѧĹ淶סƶϡͳѧ壬˵
Ǿû˼ˡԭˣҾͲˡ

ʹ־ԵݣȻѧѧƵĵķչжУѧ
о͸һ㣬ڵʷķڣʱ߶Ⱥճϰߵʱ߶
ܴĿȾͲˣһʱܽҲ⡣һ
µʱ䷶Χûǿҵʵ֤Чġ

е¼ʷ̣޷ͳƿĻԣֻ
ҹҹҲͬԭ丽ļ¼ϸ
мصʱҲǧ꣬ͳƵĽӽʵʣ
ԶҪһЩάԻΪڻش
᲻ᷢʱܺаյƲ⣺Χ
ɽ8ҵǿ240ԺӦ˵ڽڣܱ
ǲܷǿġΪйѧԺίԱʷ
1956ͽо߷ĻԵоΪ
ƻԼǿΪ30030꣬Ѿ4ظı֡

ͳʹõЩʷ¼ǹżеĵã
Ⱦѧҹʷϵĵ𣬲鵽ԭʼһǧȷ
ĵǾǧΡ

йŴע¼ΪΪǴǶԻʵ۵ľ棬
͢Ҫʷ¼۾֮صķ־˽˵ǡ¼
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ҲͲ٣ҪЩųźϿѧҪĳɷ֡

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ڶйڶļأΪǵط˵Ǿʹˣ
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ܿ󣬽е̨棬һʼء

˼ʹܸʷȷ﷢һεҪͳƣ
׼ȷظλáʱ̺𼶣ǰֵȽȷ
ѣưоҶ𼶹ϵҳʷ
ĵҶ𼶵ķܽɹʽйʷϵĵˣ
𼶾֪ϳֵĵԵʶ
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ҶǴӵԵεӰ̶Ⱥ˵ĸȷģЩ
йĵʷ¼ǱȽϷḻģӶȷĵҶȿ
ţݴҲΪѧܣư1982
ȻѧȽʽǸ鹫ʽ

ѧ˵ҪиݣſڿӡռʱеĲ
һôϤ˵ⲻҪٽˡ
һ˵ӦſѧңҪ׷ȥʸף־ҲǺõģԼ
֪Ϊѧں˵ֻʾԼ֪ǳ
Щʹƿڴʵߣĸǿˡ

̸ɽһƪBԺʿӦ200겻 ý
(ͼ)-Ѻšе⼸ԺʿߵĶԻҪ˵䡣 

籨ǰڳɶһ̳˵ɶ200ڲٷ˼
ϵĴΪʿѧңԺʿһЩɺ
Ƿ񿴹ôЩ

BҪ˵ǣýıȫҵı⡣ҲԤ˵
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оĻβУCCTV.com-ƵеĹ
ƽ ʯ"й"֣ӹ 20031210 16:45
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߶ˡƬ֮ʡһģõĶԡ桷һ
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֤Ϊ,¹ѧS. Mayer٤10췢֡ԣ
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(XYS20080702)

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ͬһ顤Ѱøĸ￪ʮҪ

ʫѡʱľɰ

Լ׫ 
й걨2008-07-01

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